Features of the clinical course of hypertrophic obstructive cardiomyopathy in a patient with extreme ventricular septal hypertrophy

Authors: Ivleva O.V., Berseneva M.I., Avdeeva M.V., Bockeria L.A.

Company: 1 Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation
2 North-Western State Medical University named after I.I. Mechnikov, Saint-Petersburg, Russian Federation
3 St. Petersburg State Pediatric Medical University, Saint-Petersburg, Russian Federation

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Type:  Case reports


DOI: https://doi.org/10.24022/1997-3187-2023-17-1-160-170

For citation: Ivleva O.V., Berseneva M.I., Avdeeva M.V., Bockeria L.A. Features of the clinical course of hypertrophic obstructive cardiomyopathy in a patient with extreme ventricular septal hypertrophy. Creative Cardiology. 2023; 17 (1): 160–70 (in Russ.). DOI: 10.24022/1997-3187-2023-17-1-160-170

Received / Accepted:  17.08.2022 / 29.03.2023

Keywords: hypertrophic obstructive cardiomyopathy SAM-syndrome



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Abstract

A rare clinical case of hypertrophic obstructive cardiomyopathy with extreme hypertrophy of the interventricular septum in a 16-year-old boy is presented. The patient complained of shortness of breath and discomfort in the retrosternal region during exercise. The examination revealed an extreme thickening of the interventricular septum up to 48 mm, obstruction in the outflow tract of the left ventricle with a pressure gradient of 110 mm Hg, unstable jogging ventricular tachycardia at night and in the morning. Considering the high risk of sudden cardiac death, an individual plan of treatment was developed for the patient.

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About Authors

  • Olga V. Ivleva, Cand. Med. Sci., Researcher; ORCID
  • Marina I. Berseneva, Cand. Med. Sci., Head of the Department; ORCID
  • Marina V. Avdeeva, Dr. Med. Sci., Professor; ORCID
  • Leo A. Boсkeria, Dr. Med. Sci., Professor, Academician of RAS, President; ORCID

Chief Editor

Leo A. Bockeria, MD, PhD, DSc, Professor, Academician of Russian Academy of Sciences, President of Bakoulev National Medical Research Center for Cardiovascular Surgery