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Cardiac sarcoma

Authors: Golukhova Е.Z., Shamsiev G.А., Kubova М.Ch., Bulaeva N.I., Efendiеva А.S., Fedenko А.А.

Company: 1 Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, 121552, Russian Federation
2 P. Hertsen Moscow Oncology Research Institute – Branch of National Medical Research Radiological Centre, Moscow, 125284, Russian Federation

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Type:  Case reports


DOI: https://doi.org/10.24022/1997-3187-2020-14-4-407-414

For citation: Golukhova Е.Z., Shamsiev G.А., Kubova М.Ch., Bulaeva N.I., Efendiеva А.S., Fedenko А.А. Cardiac sarcoma. Creative Cardiology. 2020; 14 (4): 407–14 (in Russ.). DOI: 10.24022/1997-3187-2020-14-4-407-414

Received / Accepted:  09.11.2020 / 17.11.2020

Keywords: primary heart tumors cardiac sarcoma malignant neoplasms of the heart

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Abstract

The article presents the case of primary cardiac sarcoma in a 56-year-old woman who was initially considered as a benign neoplasm. The patient was admitted without any clinical manifestations of heart or respiratory failure. A mass of the left atrium was discovered by chance. At the Bakoulev Center, the patient underwent a clinical and diagnostic examination, the results of which did not reveal any changes that made one think about the malignant transformation of the neoplasm. The patient was planned for surgical intervention to remove the mass of the left atrium. In the left atrium was found a neoplasm measuring 7 × 2 cm of dense mucous consistency, yellow-brown in color, in the capsule, prolapsing into the cavity of the left ventricle through the mitral valve. The tumor was removed. Histological analysis revealed poorly differentiated polymorphic cell sarcoma. The early postoperative period was uneventful. The patient was referred for a consultation with oncologists and is currently under the supervision of our colleagues, received 4 courses of chemotherapy. Despite advances in imaging techniques and their growing clinical availability, in most cases, malignant neoplasms of the heart are diagnosed too late. It happenes cause of nonspecificity, and sometimes the absence of symptoms. The prognosis of patient survival is no more than 12 months from the moment of diagnosis.

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About Authors

  • Elena Z. Golukhova, Dr. Med. Sc., Professor, Academician of RAS, Chief of Chair, Acting Director, Deputy Chief Editor of the Journal, ORCID
  • Gufron A. Shamsiev, Dr. Med. Sc., Leading Researcher, Cardiovascular Surgeon, ORCID
  • Maida Ch. Kubova, Researcher, Cardiologist, ORCID
  • Naida I. Bulaeva, Cand. Biol. Sc., Senior Researcher, Cardiologist, ORCID
  • Anastasiya S. Efendieva, Clinical Resident, ORCID
  • Aleksandr A. Fedenko, Dr. Med. Sc., Head of Department of Drug Treatment, ORCID

Chief Editor

Leo A. Bockeria, MD, PhD, DSc, Professor, Academician of Russian Academy of Sciences, President of Bakoulev National Medical Research Center for Cardiovascular Surgery


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