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Non-compact cardiomyopathy, manifested by acute left ventricular failure in the early postpartum period

Authors: Bliznyuk S.A., Alekseev V.G., Lyakhova N.L., Libov I.A., Komarova A.G.

Company: City Clinical Hospital named after S.P. Botkin, Moscow, Russian Federation

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Type:  Clinical Cases


DOI: https://doi.org/10.24022/1997-3187-2022-16-3-404-412

For citation: Bliznyuk S.A., Alekseev V.G., Lyakhova N.L., Libov I.A., Komarova A.G. Non-compact cardiomyopathy, manifested by acute left ventricular failure in the early postpartum period. Creative Cardiology. 2022; 16 (3): 404–12 (in Russ.). DOI: 10.24022/1997-3187-2022-16-3-404-412

Received / Accepted:  02.08.2022 / 30.08.2022

Keywords: non-compact myocardium of the left ventricle pregnancy acute left ventricular failure

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Abstract

Left ventricular non-compaction (LVNC) is a rare cardiomyopathy characterized by thickening of the endocardial layer with the formation of multiple trabeculae and intertrabecular recesses not communicate with the coronary circulation. Diagnosis of the disease is based on the results of echocardiography. In addition to echocardiography, cardiac magnetic resonance imaging is used, which is the method of choice to confirm or rule out LVNC because echocardiography cannot allow proper visualization of the apex in some cases.
The clinical picture of the disease is varied and is determined by thromboembolic syndrome, cardiac arrhythmias and heart failure. Treatment of LVNC is based on the treatment of heart failure, medical and surgical treatment of cardiac arrhythmias and the prevention of thromboembolic complications. Patients with end-stage heart failure need a cardiac transplantation.
We present a clinical case of a 38-year-old patient with acute left ventricular failure in early postpartum period due to non-compact cardiomyopathy. The prevalence of non-compact myocardium of the left ventricle in the population and among pregnant women was analyzed. Diagnostics, treatment and cardiovascular complications in this pathology were considered.

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About Authors

  • Svetlana A. Bliznyuk, Cand. Med. Sci., Head of Department, Researcher; ORCID
  • Vladimir G. Alekseev, Dr. Med. Sci., Professor, Therapist; ORCID
  • Nataliya L. Lyakhova, Cand. Med. Sci., Head of Department, Researcher, Cardiologist; ORCID
  • Igor’ A. Libov, Cand. Med. Sci., Senior Researcher; ORCID
  • Anna G. Komarova, Cand. Med. Sci., Deputy Chief Physician, Leading Researcher, Cardiologist; ORCID

Chief Editor

Leo A. Bockeria, MD, PhD, DSc, Professor, Academician of Russian Academy of Sciences, President of Bakoulev National Medical Research Center for Cardiovascular Surgery


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