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Persistent fifth aortic arch

Authors: Malozemova O.G., Gasanova R.M., Yarygina T.A., Kholmanskaya E.V., Turko Kh.R.

Company: 1 Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation
2 Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology, Moscow, Russian Federation
3 National Medical Research Center for Children’s Health, Moscow, Russian Federation

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Type:  Reviews


DOI: https://doi.org/10.24022/1997-3187-2023-17-2-227-236

For citation: Malozemova O.G., Gasanova R.M., Yarygina T.A., Kholmanskaya E.V., Turko Kh.R. Persistent fifth aortic arch. Creative Cardiology. 2023; 17 (2): 227–36 (in Russ.). DOI: 10.24022/1997-3187-2023-17-2-227-236

Received / Accepted:  05.05.2023 / 20.06.2023

Keywords: persistent fifth aortic arch double lumen aortic arch double aortic arch aortic arch anomalies congenital heart disease echocardiography

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Abstract

Persistence of the fifth aortic arch is an extremely rare and controversial congenital anomaly in the development of the main arteries and large vessels with variable anatomical shapes, which may be associated with critical congenital heart disease, accompanied by impaired systemic or pulmonary blood flow. The definition and true embryological origin of this anatomical structure is still a highly debatable issue. Therefore, persistence of the fifth aortic arch is often a diagnostic problem. We describe a clinical case demonstrating the presence of an additional arterial vessel connecting the ascending and descending aorta, which is classified in the literature as one of the possible options for preserving the 5th aortic arch. The purpose of this review is to raise awareness of this extremely rare and unusual developmental anomaly.

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About Authors

  • Olga G. Malozemova, Ultrasonic Diagnostics Physician of the Department of Ultrasound Diagnostics in Neonatology and Pediatrics, Kulakov NMRC OGP, Ultrasonic Diagnostics Physician of the Department of Ultrasound Diagnostics in Bakoulev NMRC CS; ORCID
  • Rena M. Gasanova, Dr. Med. Sci., Head of the Perinatal Cardiology Center of the Federal State Budgetary Institution Bakoulev NMRC CS, Physician of Ultrasound Diagnostics of the Department of Ultrasound and Functional Diagnostics in Kulakov NMRC OGP; ORCID
  • Tamara A. Yarygina, Cand. Med. Sci., Ultrasonic Diagnostics Physician, Researcher, ORCID
  • Elena V. Kholmanskaya, Ultrasonic Diagnostics Physician of the Department of Ultrasound Diagnostics in Bakoulev NMRC CS, Ultrasonic Diagnostics Physician of the Department of Ultrasound Diagnostics in Neonatology and Pediatrics, Kulakov NMRC OGP; ORCID
  • Khiba R. Turko, Ultrasonic Diagnostics Physician; ORCID

Chief Editor

Leo A. Bockeria, MD, PhD, DSc, Professor, Academician of Russian Academy of Sciences, President of Bakoulev National Medical Research Center for Cardiovascular Surgery


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