A modern comprehensive diagnostic and surgical approach to the correction of Bland–White–Garland syndrome and valvular insufficiency in adult patient

Authors: I.I. Skopin1, P.V. Kakhktsyan1, I.M. Tsiskaridze1, K.E. Kovalenko1, I.V. Slivneva1, I.S. Zheleznyak2, S.V. Kushnarev2

Company: 1 Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, 121552, Russian Federation
2 S.M. Kirov Military-Medical Academy, Saint-Petersburg, 194044, Russian Federation

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Type:  Case reports


DOI: https://doi.org/10.24022/1997-3187-2020-14-2-167-177

For citation: Skopin I.I., Kakhktsyan P.V., Tsiskaridze I.M., Kovalenko K.E., Slivneva I.V., Zheleznyak I.S., Kushnarev S.V. A modern comprehensive diagnostic and surgical approach to the correction of Bland-White-Garland syndrome and valvular insufficiency in adult patient. Creative Cardiology. 2020; 14 (2): 167–77 (in Russ.). DOI: 10.24022/1997-3187-2020-14-2-167-177

Received / Accepted:  20.05.2020 / 29.05.2020

Keywords: Bland–White–Garland syndrome anomalous left coronary artery from the pulmonary artery congenital heart disease 3D printing 3D modeling

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Abstract

Bland–White–Garland syndrome or abnormal origin of the left coronary artery from the pulmonary artery is a rare, usually fatal heart disease, which occurs in 0.24–0.46% of all congenital heart defects and is associated with a high mortality rate at an early age. The adult type of this pathology is even less common and is presented in the literature as particular clinical cases. Until recently, the diagnosis of this congenital anomaly was a huge problem because of lack of specific signs of the disease or the existing latent clinical picture. Due to modern research technique possibilities and accumulated data, there are more and more diagnostic signs of abnormal coronary artery origin. We carried out a modern complex of diagnostic measures using 3D printing of a heart model, aimed at choosing the most suitable technique for the surgical correction of the defect in this patient.

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About Authors

Ivan I. Skopin, Dr. Med. Sc., Professor, Head of Department, orcid.org/0000-0001-7411-202X
Pavel V. Kakhktsyan, Cand. Med. Sc., Senior Researcher, orcid.org/0000-0002-8781-5012
Irma M. Tsiskaridze, Cand. Med. Sc., Senior Researcher
Kirill E. Kovalenko, Postgraduate, orcid.org/0000-0002-3389-1714
Inessa V. Slivneva, Cand. Med. Sc., Researcher, Ultrasonic Diagnostician, orcid.org/0000-0001-7935-7093;
Igor’ S. Zheleznyak, Dr. Med. Sc., Associate Professor, Radiologist, Chief of Chair, orcid.org/0000-0001-7383-512X
Sergey V. Kushnarev, Radiologist, Adjunct, orcid.org/0000-0003-2841-2990

Chief Editor

Leo A. Bockeria, MD, PhD, DSc, Professor, Academician of Russian Academy of Sciences, Director of Bakoulev National Medical Research Center for Cardiovascular Surgery