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Diagnostic search for high pulmonary hypertension on the example of a clinical case

Authors: Grishenok A.V., Koksheneva I.V., Buziashvili V.U.

Company: Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation

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Type:  Case reports


DOI: https://doi.org/10.24022/1997-3187-2021-15-3-407-417

For citation: Grishenok A.V., Koksheneva I.V., Buziashvili V.Yu. Diagnostic search for high pulmonary hypertension on the example of a clinical case. Creative Cardiology. 2021; 15 (3): 407–17 (in Russ.). DOI: 10.24022/1997-3187-2021-15-3-407-417

Received / Accepted:  08.08.2021 / 06.09.2021

Keywords: pulmonary hypertension connective tissue disease systemic sclerosis interstitial lung disease

Full text:  

 

Abstract

The article provides diagnostic investigation of a clinical case of a patient with high pulmonary hypertension, possible pulmonary embolism, primary lung disease and connective tissue disease. We have diagnosed pulmonary hypertension associated with systemic sclerosis. Although, the pulmonary hypertension may have been caused by combination of several reasons, including possible chronic pulmonary embolism, comorbid lung diseases, Raynaud's syndrome; only scleroderma was definitively diagnosed. The patient's age and co-morbidities have caused the difficulty during diagnostic investigation. The clinical manifestation of pulmonary hypertension was presented only by dyspnea, which required differential diagnosis with a wide range of conditions, caused either by systemic sclerosis or conditions associated with it.

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About Authors

  • Alena V. Grishenok, Postgraduate; ORCID
  • Inna V. Koksheneva, Dr. Med. Sci., Senior Researcher; ORCID
  • Viktoria Yu. Buziashvili, Сand. Med. Sci., Junior Researcher; ORCID

Chief Editor

Leo A. Bockeria, MD, PhD, DSc, Professor, Academician of Russian Academy of Sciences, President of Bakoulev National Medical Research Center for Cardiovascular Surgery


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